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Table 4 Clinical and demographic descriptors for each of the c-SLE malignancy cases

From: Childhood-onset systemic lupus erythematosus (cSLE) and malignancy: a nationwide multicentre series review

Demographic and clinical characteristics

c-SLE Cases

 

1

2

3

4

5

6

7

8

9

10

11

12

Median (min–max)

Age at malignancy diagnosis (years)

24

14

12

16

15

13

32

30

27

32

27

22

23 (12–32)

Age at cSLE diagnosis

10

14

11

10

11

12

13

17

12

16

12

13

12 (10–17)

cSLE duration (years)

14

0.2

1.8

6.1

4

1.3

19

13

16

16

12

8.7

10 (0.2–19)

Gender (F:M)

F

F

F

F

M

F

F

F

F

F

F

F

11:1

Specific Malignancy

SC

HL

NHL

NHL

TT

OL

AC

ALL

SC

SC

SC

C

SLEDAI 2K scores

22

31

13

10

4

38

8

1

3

0

12

7

9 (0–38)

SLICC/ACR-DI scores

5

1

1

1

1

1

1

1

1

2

2

1 (1–5)

Drugs ever used during c-SLE follow up

PDN

MPDN

HXC

MMF

AZA

CYC

RTX

PDN

MPDN

HXC MMF

AZA

PDN

HXC

AZA

PDN

HXC AZA

PDN

MPDN

HXC AZA

MMF

CYC

IVIG

PDN

HXC

PDN

HXC UNK

HXC

UNK

PDN

UNK

HXC MMF

UNK

PDN

HXC MMF

UNK

PDN

HXC

MTX

 
  1. ALL, Acute lymphoblastic leukemia; AC, Adenocarcinoma; AZA, Azathioprine; c-SLE, childhood onset systemic lupus erythematosus; C, Carcinoid; CYC, Cyclophosphamide; HK, Hodgkin lymphoma; HXC, Hydroxychloroquine; IVIG, Intravenous Immunoglobulin; MTX, Methotrexate; MPDN, Methylprednisolone pulse; MMF, Mofetil mycophenolate; NHL, Non Hodgkin lymphoma; OL, Oligodendroglioma; PDN, Prednisone; RTX, Rituximab; SC, Squamous carcinoma; SLEDAI-2K, Systemic Lupus Erythematosus Disease Activity Index 2000; SLICC/ACR-DI, Systemic Lupus International Collaborating Clinics (SLICC)/American College of Rheumatology (ACR) Damage Index (SDI); TT, Gonadal Teratoma; UNK, Unknown data