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Table 1 Box 1: RP diagnostic criteria [19,20,21]

From: Unveiling the clinical spectrum of relapsing polychondritis: insights into its pathogenesis, novel monogenic causes, and therapeutic strategies

Authors

Criteria

Conditions required

McAdam et al.

Bilateral auricular chondritis

Nasal chondritis

Respiratory tract chondritis

Non-erosive seronegative polyarthritis

Occular inflammation

Audiovestibular damage

3 out of 6 criteria

Damiani et al.

Bilateral auricular chondritis (A)

Nasal cartilage inflammation (A)

Respiratory tract chondritis (A)

Non-erosive seronegative polyarthritis (A)

Occular inflammation (A)

Audiovestibular damage (A)

Histologic confirmation (B)

Positive response to corticosteroids or dapsone (C)

3 (A) criteria or

1 (A) and (B) or

2 (A) criteria and (C)

Michet et al.

Auricular cartilage inflammation (A)

Nasal cartilage inflammation (A)

Laryngotracheal cartilage inflammation (A)

Ocular inflammation (B)

Hearing loss(B)

Vestibulary dysfunction (B)

Sero-negative arthritis (B)

2 out of 3 (A) criteria or

1 out of 3 (A) criteria and 2 (B) criteria